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Leukocyte Adhesion Defect Type 1 Presenting with Recurrent Pyoderma Gangrenosum

Leukocyte adhesion deficiency 1 (LAD-1) is a rare autosomal recessive disorder of leukocyte function. LAD-1 affects about 1 per 10 million individuals and is characterized by recurrent bacterial and fungal infections and depressed inflammatory responses despite striking blood neutrophilia. Patients...

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Hlavní autoři: Thakur, Neha, Sodani, Ravitanya, Chandra, Jagdish, Singh, Varinder
Médium: Artigo
Jazyk:Inglês
Vydáno: Medknow Publications & Media Pvt Ltd 2013
Témata:
On-line přístup:https://ncbi.nlm.nih.gov/pmc/articles/PMC3657233/
https://ncbi.nlm.nih.gov/pubmed/23716823
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.4103/0019-5154.108076
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