Carregant...

Selective reduction of bis(monoacylglycero)phosphate ameliorates the storage burden in a THP-1 macrophage model of Gaucher disease

Bis(monoacylglycero)phosphate (BMP) assists lysosomal function by facilitating interaction of hydrolases and activator proteins with sphingolipid substrates. Impaired lysosomal degradation of the sphingolipid glucosylceramide (GC) occurs in Gaucher disease due to an inherited deficiency of acid β-gl...

Descripció completa

Guardat en:
Dades bibliogràfiques
Autors principals: Hein, Leanne K., Duplock, Stephen, Fuller, Maria
Format: Artigo
Idioma:Inglês
Publicat: The American Society for Biochemistry and Molecular Biology 2013
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC3646469/
https://ncbi.nlm.nih.gov/pubmed/23564732
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1194/jlr.M038232
Etiquetes: Afegir etiqueta
Sense etiquetes, Sigues el primer a etiquetar aquest registre!