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Quantitative Measurement of Urinary Excretion of 3-Hydroxyisovaleryl Carnitine by LC–MS/MS as an Indicator of Biotin Status in Humans

Abnormally increased urinary excretion of 3-hydroxyisovaleryl carnitine (3HIA-carnitine) results from impairment in leucine catabolism caused by reduced activity of the biotin-dependent enzyme 3-methylcrotonyl-CoA carboxylase. Accordingly, urinary 3HIA-carnitine might reflect biotin status. Here, we...

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Autores principales: Horvath, Thomas D., Stratton, Shawna L., Bogusiewicz, Anna, Owen, Suzanne N., Mock, Donald M., Moran, Jeffery H.
Formato: Artigo
Lenguaje:Inglês
Publicado: 2010
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC3643005/
https://ncbi.nlm.nih.gov/pubmed/21028833
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1021/ac102330k
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