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A Polycystin-1 Multiprotein Complex Is Disrupted in Polycystic Kidney Disease Cells

Autosomal dominant polycystic kidney disease (ADPKD) is typified by the accumulation of fluid-filled cysts and abnormalities in renal epithelial cell function. The disease is principally caused by mutations in the gene encoding polycystin-1, a large basolateral plasma membrane protein expressed in k...

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Autors principals: Roitbak, Tamara, Ward, Christopher J., Harris, Peter C., Bacallao, Robert, Ness, Scott A., Wandinger-Ness, Angela
Format: Artigo
Idioma:Inglês
Publicat: The American Society for Cell Biology 2004
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Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC363138/
https://ncbi.nlm.nih.gov/pubmed/14718571
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1091/mbc.E03-05-0296
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