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Characterization of Connective Tissue Disease-Associated Pulmonary Arterial Hypertension From REVEAL: Identifying Systemic Sclerosis as a Unique Phenotype

BACKGROUND: REVEAL (the Registry to Evaluate Early and Long-term Pulmonary Arterial Hypertension Disease Management) is the largest US cohort of patients with pulmonary arterial hypertension (PAH) confirmed by right-sided heart catheterization (RHC), providing a more comprehensive subgroup character...

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Autori principali: Chung, Lorinda, Liu, Juliana, Parsons, Lori, Hassoun, Paul M., McGoon, Michael, Badesch, David B., Miller, Dave P., Nicolls, Mark R., Zamanian, Roham T.
Natura: Artigo
Lingua:Inglês
Pubblicazione: American College of Chest Physicians 2010
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC3621419/
https://ncbi.nlm.nih.gov/pubmed/20507945
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1378/chest.10-0260
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