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Acute Pancreatitis with Rapid Clinical Improvement in a Child with Isovaleric Acidemia

Isovaleric acidemia is a rare branched-chain organic acidemia. The authors describe a 3.5-year-old girl with isovaleric acidemia and acute abdominal pain associated with bilious emesis. Elevated serum amylase and abdominal ultrasonography demonstrating an enlarged and edematous pancreas, along with...

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Detalhes bibliográficos
Main Authors: Mantadakis, Elpis, Chrysafis, Ioannis, Tsouvala, Emmanouela, Evangeliou, Athanassios, Chatzimichael, Athanassios
Formato: Artigo
Idioma:Inglês
Publicado em: Hindawi Publishing Corporation 2013
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC3575664/
https://ncbi.nlm.nih.gov/pubmed/23431490
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1155/2013/721871
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