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Proteomics reveals drastic increase of extracellular matrix proteins collagen and dermatopontin in the aged mdx diaphragm model of Duchenne muscular dystrophy

Duchenne muscular dystrophy is a lethal genetic disease of childhood caused by primary abnormalities in the gene coding for the membrane cytoskeletal protein dystrophin. The mdx mouse is an established animal model of various aspects of X-linked muscular dystrophy and is widely used for studying fun...

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Autori principali: CARBERRY, STEVEN, ZWEYER, MARGIT, SWANDULLA, DIETER, OHLENDIECK, KAY
Natura: Artigo
Lingua:Inglês
Pubblicazione: D.A. Spandidos 2012
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC3573751/
https://ncbi.nlm.nih.gov/pubmed/22614334
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3892/ijmm.2012.1006
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