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Spectrum of NIPBL gene mutations in Polish patients with Cornelia de Lange syndrome

Cornelia de Lange syndrome (CdLS) is a rare multi-system genetic disorder characterised by growth and developmental delay, distinctive facial dysmorphism, limb malformations and multiple organ defects. The disease is caused by mutations in genes responsible for the formation and regulation of cohesi...

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Main Authors: Kuzniacka, Alina, Wierzba, Jolanta, Ratajska, Magdalena, Lipska, Beata S., Koczkowska, Magdalena, Malinowska, Monika, Limon, Janusz
Formato: Artigo
Idioma:Inglês
Publicado: Springer-Verlag 2012
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Acceso en liña:https://ncbi.nlm.nih.gov/pmc/articles/PMC3548104/
https://ncbi.nlm.nih.gov/pubmed/23254390
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1007/s13353-012-0126-9
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