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Idiopathic pleuroparenchymal fibroelastosis: consideration of a clinicopathological entity in a series of Japanese patients

BACKGROUND: Idiopathic pleuroparenchymal fibroelastosis (IPPFE) is a recently reported group of disorders characterized by fibrotic thickening of the pleural and subpleural parenchyma predominantly in the upper lobes. We report five Japanese cases fulfilling the criteria of IPPFE and address whether...

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Autors principals: Kusagaya, Hideki, Nakamura, Yutaro, Kono, Masato, Kaida, Yusuke, Kuroishi, Shigeki, Enomoto, Noriyuki, Fujisawa, Tomoyuki, Koshimizu, Naoki, Yokomura, Koshi, Inui, Naoki, Suda, Takafumi, Colby, Thomas V, Chida, Kingo
Format: Artigo
Idioma:Inglês
Publicat: BioMed Central 2012
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Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC3539991/
https://ncbi.nlm.nih.gov/pubmed/23216996
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/1471-2466-12-72
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