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Mechanisms of CFTR Folding at the Endoplasmic Reticulum

In the past decade much has been learned about how Cystic Fibrosis Transmembrane Conductance Regulator (CFTR) folds and misfolds as the etiologic cause of cystic fibrosis (CF). CFTR folding is complex and hierarchical, takes place in multiple cellular compartments and physical environments, and invo...

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Detalhes bibliográficos
Main Authors: Kim, Soo Jung, Skach, William R.
Formato: Artigo
Idioma:Inglês
Publicado em: Frontiers Media S.A. 2012
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC3521238/
https://ncbi.nlm.nih.gov/pubmed/23248597
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3389/fphar.2012.00201
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