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457 Clinical Features and Outcome of 82 Patients with Hereditary Angioedema

BACKGROUND: Hereditary angioedema due to C1 inhibitor deficiency is clinically characterized by relapsing skin and mucosal swelling, abdominal pain and life threatening upper airway obstruction. It still is a disease poor known by physicians and underdiagnosed. METHODS: We analyzed the clinical feat...

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Detalhes bibliográficos
Main Authors: D'Ottaviano, Fabricio Loffredo, Giavina-Bianchi, Pedro, Motta, Antonio Abilio, Aun, Marcelo Vivolo
Formato: Artigo
Idioma:Inglês
Publicado em: World Allergy Organization Journal 2012
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC3512745/
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1097/01.WOX.0000411572.66572.a4
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