A defect in the structure of type I procollagen in a patient who had osteogenesis imperfecta: excess mannose in the COOH-terminal propeptide.

Fibroblasts from normal human subjects and from a patient who had osteogenesis imperfecta were incubated with [3H]mannose, and types I and III procollagens were isolated from the culture medium. The type I procollagen from the patient's fibroblasts contained 2-3 time more [3H]mannose than the t...

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Bibliografiska uppgifter
Huvudupphovsmän: Peltonen, L, Palotie, A, Prockop, D J
Materialtyp: Artigo
Språk:Inglês
Publicerad: 1980
Ämnen:
Research Article
Länkar:https://ncbi.nlm.nih.gov/pmc/articles/PMC350238/
https://ncbi.nlm.nih.gov/pubmed/6934545
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