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Hyper IgM syndrome presenting as chronic suppurative lung disease

The Hyper-immunoglobulin M syndromes (HIGM) are a heterogeneous group of genetic disorders resulting in defects of immunoglobulin class switch recombination. Affected patients show humoral immunodeficiency and high susceptibility to opportunistic infections. Elevated serum IgM levels are the hallmar...

Täydet tiedot

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Bibliografiset tiedot
Päätekijät: Montella, Silvia, Maglione, Marco, Giardino, Giuliana, Di Giorgio, Angela, Palamaro, Loredana, Mirra, Virginia, Ursini, Matilde Valeria, Salerno, Mariacarolina, Pignata, Claudio, Caffarelli, Carlo, Santamaria, Francesca
Aineistotyyppi: Artigo
Kieli:Inglês
Julkaistu: BioMed Central 2012
Aiheet:
Linkit:https://ncbi.nlm.nih.gov/pmc/articles/PMC3484017/
https://ncbi.nlm.nih.gov/pubmed/22992442
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/1824-7288-38-45
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