Učitavanje...

Lipoid proteinosis in a six-year-old child

Lipoid proteinosis (LiP) (OMIM 247100) is a rare autosomal recessive disease caused by loss of function mutations in the extracellular matrix protein 1 gene, ECM1, on chromosome 1q21. Clinically characterized by hoarseness in early infancy, followed by waxy papules and plaques on the face and body a...

Cijeli opis

Spremljeno u:
Bibliografski detalji
Glavni autori: Nayak, Surajit, Acharjya, Basanti
Format: Artigo
Jezik:Inglês
Izdano: Medknow Publications & Media Pvt Ltd 2012
Teme:
Online pristup:https://ncbi.nlm.nih.gov/pmc/articles/PMC3481908/
https://ncbi.nlm.nih.gov/pubmed/23130256
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.4103/2229-5178.93490
Oznake: Dodaj oznaku
Bez oznaka, Budi prvi tko označuje ovaj zapis!