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Aquaporin-4 expression in distal myopathy with rimmed vacuoles

BACKGROUND: Distal myopathy with rimmed vacuoles/hereditary inclusion body myopathy is clinically characterized by the early involvement of distal leg muscles. The striking pathological features of the myopathy are muscle fibers with rimmed vacuoles. To date, the role of aquaporin-4 water channel in...

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Hlavní autoři: Hoshi, Akihiko, Yamamoto, Teiji, Kikuchi, Saeko, Soeda, Tomoko, Shimizu, Keiko, Ugawa, Yoshikazu
Médium: Artigo
Jazyk:Inglês
Vydáno: BioMed Central 2012
Témata:
On-line přístup:https://ncbi.nlm.nih.gov/pmc/articles/PMC3477015/
https://ncbi.nlm.nih.gov/pubmed/22540328
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/1471-2377-12-22
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