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Absence of the cystic fibrosis transmembrane regulator (Cftr) from myeloid-derived cells slows resolution of inflammation and infection

The absence or reduction of CFTR function causes CF and results in a pulmonary milieu characterized by bacterial colonization and unresolved inflammation. The ineffectiveness at controlling infection by species such as Pseudomonas aeruginosa suggests defects in innate immunity. Macrophages, neutroph...

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Autori principali: Bonfield, T. L., Hodges, C. A., Cotton, C. U., Drumm, M. L.
Natura: Artigo
Lingua:Inglês
Pubblicazione: Society for Leukocyte Biology 2012
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC3476241/
https://ncbi.nlm.nih.gov/pubmed/22859830
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1189/jlb.0412188
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