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Liver Transplantation for Acute Intermittent Porphyria is Complicated by a High Rate of Hepatic Artery Thrombosis

Acute intermittent porphyria (AIP) is an autosomal-dominant condition resulting from a partial deficiency of the ubiquitously expressed enzyme porphobilinogen deaminase. Although its clinical expression is highly variable, a minority of patients suffer recurrent life-threatening neurovisceral attack...

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Autores principales: Dowman, Joanna K, Gunson, Bridget K, Mirza, Darius F, Bramhall, Simon R, Badminton, Mike N, Newsome, Philip N
Formato: Artigo
Lenguaje:Inglês
Publicado: Wiley Subscription Services, Inc., A Wiley Company 2012
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC3472026/
https://ncbi.nlm.nih.gov/pubmed/21618697
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1002/lt.22345
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