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Impaired Osteoblastogenesis in a Murine Model of Dominant Osteogenesis Imperfecta: A New Target for Osteogenesis Imperfecta Pharmacological Therapy

The molecular basis underlying the clinical phenotype in bone diseases is customarily associated with abnormal extracellular matrix structure and/or properties. More recently, cellular malfunction has been identified as a concomitant causative factor and increased attention has focused on stem cells...

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Detalhes bibliográficos
Main Authors: Gioia, Roberta, Panaroni, Cristina, Besio, Roberta, Palladini, Giovanni, Merlini, Giampaolo, Giansanti, Vincenzo, Scovassi, Ivana A., Villani, Simona, Villa, Isabella, Villa, Anna, Vezzoni, Paolo, Tenni, Ruggero, Rossi, Antonio, Marini, Joan C., Forlino, Antonella
Formato: Artigo
Idioma:Inglês
Publicado em: 2012
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Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC3459187/
https://ncbi.nlm.nih.gov/pubmed/22511244
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1002/stem.1107
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