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Interallelic complementation in an inborn error of metabolism: genetic heterogeneity in argininosuccinate lyase deficiency.

We used complementation analysis as a probe for the detection of genetic heterogeneity within a single locus affected in a human disease, argininosuccinate lyase (L-argininosuccinate arginine-lyase, EC 4.3.2.1) deficiency. Fibroblasts cultured from 28 unrelated patients were fused in all possible pa...

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Detaylı Bibliyografya
Asıl Yazarlar: McInnes, R R, Shih, V, Chilton, S
Materyal Türü: Artigo
Dil:Inglês
Baskı/Yayın Bilgisi: 1984
Konular:
Online Erişim:https://ncbi.nlm.nih.gov/pmc/articles/PMC345614/
https://ncbi.nlm.nih.gov/pubmed/6589607
Etiketler: Etiketle
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