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X-linked adreno leukodistrophy: Profiles of very long chain fatty acids in plasma and fibroblasts in eigth Serbian patients

X-linked adrenoleukodistrophy is a severe neurodegenerative disorder with impaired very long chain fatty acid metabolism. The disease associated ABCD1 gene encodes a peroxisomal membrane protein which belongs to the superfamily of ATP-binding cassette transporters. We investigated eight male X-ALD p...

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Bibliografski detalji
Glavni autori: Grkovic, Sanja, Nikolic, Rajko, Djordjevic, Maja, Stojanov, Ljubomir, Zivancevic-Simonovic, Snezana, Djordjevic-Denic, Gordana, Kecman, Bozica
Format: Artigo
Jezik:Inglês
Izdano: Springer India 2007
Teme:
Online pristup:https://ncbi.nlm.nih.gov/pmc/articles/PMC3453796/
https://ncbi.nlm.nih.gov/pubmed/23105697
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1007/BF02913328
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