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A Rare Clinical Presentation of Intraoral Darier's Disease

Darier's disease, also known as keratosis follicularis or dyskeratosis follicularis, is a rare disorder of keratinization. It is an autosomal dominant genodermatosis with high penetrance and variable expressivity. Its manifestation appears as hyperkeratotic papules primarily affecting seborrhei...

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Bibliografiske detaljer
Main Authors: Manoja, K. G. D., Siriwardena, B. S. M. S., Jayasooriya, P. R., Siriwardane, D. J. L., Tilakaratne, W. M.
Format: Artigo
Sprog:Inglês
Udgivet: Hindawi Publishing Corporation 2011
Fag:
Online adgang:https://ncbi.nlm.nih.gov/pmc/articles/PMC3420676/
https://ncbi.nlm.nih.gov/pubmed/22937379
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1155/2011/181728
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