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Birt-Hogg-Dubé syndrome: Report of a new mutation

Birt-Hogg-Dubé syndrome is an autosomal dominant genodermatosis caused by germline mutations in the folliculin gene and characterized by facial papules, pulmonary cysts, kidney tumours and recurrent pneumothoraces. Several distinct mutations in the folliculin gene resulting in a truncated protein ha...

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Detalles Bibliográficos
Autor principal: Rehman, Habib U
Formato: Artigo
Lenguaje:Inglês
Publicado: Pulsus Group Inc 2012
Materias:
Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC3418093/
https://ncbi.nlm.nih.gov/pubmed/22679611
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