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Role of the cystic fibrosis transmembrane conductance regulator in innate immunity to Pseudomonas aeruginosa infections

Chronic Pseudomonas aeruginosa infection occurs in 75–90% of patients with cystic fibrosis (CF). It is the foremost factor in pulmonary function decline and early mortality. A connection has been made between mutant or missing CF transmembrane conductance regulator (CFTR) in lung epithelial cell mem...

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Autor principal: Pier, Gerald B.
Format: Artigo
Idioma:Inglês
Publicat: The National Academy of Sciences 2000
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC34018/
https://ncbi.nlm.nih.gov/pubmed/10922041
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