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Lymphangioleiomyomatosis: what do we know and what are we looking for?

Lymphangioleiomyomatosis (LAM) is a rare disease characterised by proliferation of abnormal smooth muscle-like cells (LAM cells) leading to progressive cystic destruction of the lung, lymphatic abnormalities and abdominal tumours. It affects predominantly females and can occur sporadically or in pat...

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Detalles Bibliográficos
Autores principales: Harari, S., Torre, O., Moss, J.
Formato: Artigo
Lenguaje:Inglês
Publicado: European Respiratory Society 2011
Materias:
Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC3386525/
https://ncbi.nlm.nih.gov/pubmed/21357890
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1183/09059180.00011010
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