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Anesthetic management in children with Hurler's syndrome undergoing emergency ventriculoperitoneal shunt surgery

Mucopolysaccharidoses (MPSs) are a group of lysosomal storage disorder characterized by progressive multiorgan accumulation of glycosaminoglycans. Patients with MPS I (Hurler's syndrome) present as one of the most difficult airway problems to be managed by anesthesiologists. Hydrocephalus with...

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Dettagli Bibliografici
Autori principali: Gupta, Nidhi, Rath, Girija Prasad, Bala, Renu, Reddy, Bapura Kiran, Chaturvedi, Arvind
Natura: Artigo
Lingua:Inglês
Pubblicazione: Medknow Publications & Media Pvt Ltd 2012
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC3385265/
https://ncbi.nlm.nih.gov/pubmed/22754449
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.4103/1658-354X.97036
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