Načítá se...

TDP-43 Pathology in a Case of Hereditary Spastic Paraplegia with a NIPA1/SPG6 Mutation

Mutations in NIPA1 (non-imprinted in Prader-Willi/Angelman syndrome) have been described as a cause of autosomal dominant hereditary spastic paraplegia (HSP) known as SPG6 (spastic paraplegia-6). We present the first neuropathological description of a patient with a NIPA1 mutation, and clinical phen...

Celý popis

Uloženo v:
Podrobná bibliografie
Hlavní autoři: Martinez-Lage, Maria, Molina-Porcel, Laura, Falcone, Dana, McCluskey, Leo, Lee, Virginia M.-Y., Van Deerlin, Vivianna M., Trojanowski, John Q.
Médium: Artigo
Jazyk:Inglês
Vydáno: 2012
Témata:
On-line přístup:https://ncbi.nlm.nih.gov/pmc/articles/PMC3361549/
https://ncbi.nlm.nih.gov/pubmed/22302102
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1007/s00401-012-0947-y
Tagy: Přidat tag
Žádné tagy, Buďte první, kdo otaguje tento záznam!