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Hemin Augments Growth and Hemoglobinization of Erythroid Precursors from Patients with Diamond-Blackfan Anemia

Diamond-Blackfan anemia (DBA) is congenital pure red-cell anemia due to a differentiation block in erythroid precursors. The disease is commonly caused by mutations in genes for ribosomal proteins. Despite the identification of disease causal genes, the disease pathogenesis is not completely elucida...

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Detalhes bibliográficos
Main Authors: Fibach, Eitan, Aker, Memet
Formato: Artigo
Idioma:Inglês
Publicado em: Hindawi Publishing Corporation 2012
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC3359667/
https://ncbi.nlm.nih.gov/pubmed/22655180
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1155/2012/940260
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