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The mucopolysaccharidoses (a review).

The mucopolysaccharidoses are a group of genetic diseases characterized by storage of incompletely degraded glycosaminoglycans. Such storage causes marked distortion of many tissues with consequent severe somatic changes and mental retardation. Storage of glycosaminoglycans results from markedly dim...

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Salvato in:
Dettagli Bibliografici
Autori principali: Dorfman, A, Matalon, R
Natura: Artigo
Lingua:Inglês
Pubblicazione: 1976
Soggetti:
Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC335965/
https://ncbi.nlm.nih.gov/pubmed/813230
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