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Menkes disease: a biochemical abnormality in cultured human fibroblasts.

Cultured skin fibroblasts from patients with Menkes disease, an X-linked disorder involving a defect in copper metabolism, were analyzed for copper concentration by means of atomic absorption spectrophotometry. These cultures consistently exhibited elevated copper concentrations (mean = 335.5 ng of...

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Bibliographic Details
Main Authors: Goka, T J, Stevenson, R E, Hefferan, P M, Howell, R R
Format: Artigo
Language:Inglês
Published: 1976
Subjects:
Online Access:https://ncbi.nlm.nih.gov/pmc/articles/PMC335959/
https://ncbi.nlm.nih.gov/pubmed/1061160
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