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Bergmann Glial S100B Activates Myo-inositol Monophosphatase 1 and Co-localizes to Purkinje Cell Vacuoles in SCA1 Transgenic Mice

Spinocerebellar ataxia-1 (SCA1) is a late onset neurodegenerative disease caused by the expansion of a polyglutamine repeat within ataxin-1 protein. The toxic effects triggered by mutant ataxin-1 result in degeneration of the neurons in cerebellum, brain stem and spinocerebellar tracts. The targeted...

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Autores principales: Vig, Parminder J. S., Shao, Qingmei, Subramony, S. H., Lopez, Mariper E., Safaya, Eshan
Formato: Artigo
Lenguaje:Inglês
Publicado: 2009
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC3351107/
https://ncbi.nlm.nih.gov/pubmed/19593677
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1007/s12311-009-0125-5
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