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A high throughput glucocerebrosidase assay using the natural substrate glucosylceramide

Glucocerebrosidase is a lysosomal enzyme that catalyzes the hydrolysis of glucosylceramide to form ceramide and glucose. A deficiency of lysosomal glucocerebrosidase due to genetic mutations results in Gaucher disease, in which glucosylceramide accumulates in the lysosomes of certain cell types. Alt...

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Autores principales: Motabar, Omid, Goldin, Ehud, Leister, William, Liu, Ke, Southall, Noel, Huang, Wenwei, Marugan, Juan J., Sidransky, Ellen, Zheng, Wei
Formato: Artigo
Lenguaje:Inglês
Publicado: 2011
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC3351006/
https://ncbi.nlm.nih.gov/pubmed/22033823
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1007/s00216-011-5496-z
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