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Anesthetic management of a child with Hunter's syndrome

Hunter's syndrome is a member of a group of recessively inherited metabolic disorders termed mucopolysaccharidoses, caused by deficiency of lysosomal enzymes required for degradation of mucopolysaccharides or glycosaminoglycans, leading to accumulation of partially degraded glycosaminoglycans i...

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Autori principali: Kaur, Jasmeet, Swami, Adarsh C, Kumar, Amit, Lata, Sneh
Natura: Artigo
Lingua:Inglês
Pubblicazione: Medknow Publications & Media Pvt Ltd 2012
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC3339739/
https://ncbi.nlm.nih.gov/pubmed/22557757
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.4103/0970-9185.94914
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