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Rib Cage Deformities Alter Respiratory Muscle Action and Chest Wall Function in Patients with Severe Osteogenesis Imperfecta

BACKGROUND: Osteogenesis imperfecta (OI) is an inherited connective tissue disorder characterized by bone fragility, multiple fractures and significant chest wall deformities. Cardiopulmonary insufficiency is the leading cause of death in these patients. METHODS: Seven patients with severe OI type I...

Täydet tiedot

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Bibliografiset tiedot
Päätekijät: LoMauro, Antonella, Pochintesta, Simona, Romei, Marianna, D'Angelo, Maria Grazia, Pedotti, Antonio, Turconi, Anna Carla, Aliverti, Andrea
Aineistotyyppi: Artigo
Kieli:Inglês
Julkaistu: Public Library of Science 2012
Aiheet:
Linkit:https://ncbi.nlm.nih.gov/pmc/articles/PMC3338769/
https://ncbi.nlm.nih.gov/pubmed/22558284
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1371/journal.pone.0035965
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