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In vitro molecular reconstitution of the respiratory burst in B lymphoblasts from p47-phox-deficient chronic granulomatous disease.

Epstein-Barr virus-transformed lymphocytes generate superoxide in response to various agonists in an enzymatic reaction similar to that which occurs in stimulated phagocytes. We generated transformed B lymphoblast cell lines from controls, from four patients with p47-phox-deficient chronic granuloma...

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Detalhes bibliográficos
Publicado no:J Clin Invest
Principais autores: Volpp, B D, Lin, Y
Formato: Artigo
Idioma:Inglês
Publicado em: American Society for Clinical Investigation 1993
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.govhttps://pmc.ncbi.nlm.nih.gov/articles/PMC330015/
https://ncbi.nlm.nih.govhttps://pubmed.ncbi.nlm.nih.gov/7678602/
https://ncbi.nlm.nih.govhttps://doi.org/10.1172/JCI116171
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