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Spontaneous Thrombosis of an Orbital Arteriovenous Malformation Revealing Hereditary Haemorrhagic Telangiectasia (Rendu-Osler-Weber Disease): A Case Report

Hereditary Haemorrhagic Telangiectasia (HHT) is a genetic disorder responsible for cutaneous or mucosal telangiectasia and arteriovenous malformations (AVMs). The most frequent locations are lung and brain. In contrast, orbital AVMs are very rare. We describe a case of symptomatic orbital arterioven...

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Autors principals: Van Went, C., Ozanne, A., Saliou, G., Dethorey, G., De Monchy, I., Krings, T., Ducreux, D., Labetoulle, M.
Format: Artigo
Idioma:Inglês
Publicat: Centauro S.r.l. 2011
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Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC3296507/
https://ncbi.nlm.nih.gov/pubmed/22192551
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