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Striatal necrosis in type 1 glutaric aciduria: Different stages in two siblings

Two siblings born of a consanguineous marriage with history of neurologic deterioration were imaged. Imaging features are classical of glutaric aciduria type 1 (GA-1), acute (striatal necrosis) stage in younger sibling, and chronic stage in older sibling. GA-1 is an autosomal recessive disease with...

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Autors principals: Sen, Anitha, Pillay, Rajesh Subramonia
Format: Artigo
Idioma:Inglês
Publicat: Medknow Publications & Media Pvt Ltd 2011
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC3296414/
https://ncbi.nlm.nih.gov/pubmed/22408669
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.4103/1817-1745.92845
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