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Hyperimmunoglobulin E Syndromes in Pediatrics

PURPOSE OF REVIEW: The hyper-IgE syndromes (HIES) are primary immunodeficiencies (PID) characterized by eczema, sinopulmonary infections, and elevated serum IgE. This review discusses the clinical similarities and differences between the autosomal dominant (AD-HIES) and autosomal recessive (AR-HIES)...

Disgrifiad llawn

Wedi'i Gadw mewn:
Manylion Llyfryddiaeth
Prif Awduron: Zhang, Qian, Su, Helen C.
Fformat: Artigo
Iaith:Inglês
Cyhoeddwyd: 2011
Pynciau:
Mynediad Ar-lein:https://ncbi.nlm.nih.gov/pmc/articles/PMC3294453/
https://ncbi.nlm.nih.gov/pubmed/21970826
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1097/MOP.0b013e32834c7f65
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