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JUVENILE HYALINE FIBROMATOSIS

Juvenile hyaline fibromatosis is a rare, autosomal-recessive disease characterized by papular and nodular skin lesions, gingival hyperplasia, joint contractures and bone involvement in variable degrees. It is a connective tissue disorder with aberrant synthesis of glycosaminoglycans by fibroblasts....

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Detalhes bibliográficos
Main Authors: Krishnamurthy, Jayashree, Dalal, Bibhas Saha, Sunila, Gubanna, Manjunath V
Formato: Artigo
Idioma:Inglês
Publicado em: Medknow Publications & Media Pvt Ltd 2011
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC3276908/
https://ncbi.nlm.nih.gov/pubmed/22345782
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.4103/0019-5154.91840
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