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JUVENILE HYALINE FIBROMATOSIS

Juvenile hyaline fibromatosis is a rare, autosomal-recessive disease characterized by papular and nodular skin lesions, gingival hyperplasia, joint contractures and bone involvement in variable degrees. It is a connective tissue disorder with aberrant synthesis of glycosaminoglycans by fibroblasts....

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Autores principales: Krishnamurthy, Jayashree, Dalal, Bibhas Saha, Sunila, Gubanna, Manjunath V
Formato: Artigo
Lenguaje:Inglês
Publicado: Medknow Publications & Media Pvt Ltd 2011
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC3276908/
https://ncbi.nlm.nih.gov/pubmed/22345782
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.4103/0019-5154.91840
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