Cargando...

Dysferlin-deficient immortalized human myoblasts and myotubes as a useful tool to study dysferlinopathy

Dysferlin gene mutations causing LGMD2B are associated with defects in muscle membrane repair. Four stable cell lines have been established from primary human dysferlin-deficient myoblasts harbouring different mutations in the dysferlin gene. We have compared immortalized human myoblasts and myotube...

Descrición completa

Gardado en:
Detalles Bibliográficos
Main Authors: Philippi, Susanne, Bigot, Anne, Marg, Andreas, Mouly, Vincent, Spuler, Simone, Zacharias, Ute
Formato: Artigo
Idioma:Inglês
Publicado: Public Library of Science 2012
Assuntos:
Acceso en liña:https://ncbi.nlm.nih.gov/pmc/articles/PMC3274833/
https://ncbi.nlm.nih.gov/pubmed/22367358
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1371/currents.RRN1298
Tags: Engadir etiqueta
Sen Etiquetas, Sexa o primeiro en etiquetar este rexistro!