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TRIM32 Regulates Skeletal Muscle Stem Cell Differentiation and Is Necessary for Normal Adult Muscle Regeneration

Limb girdle muscular dystrophy type 2H (LGMD2H) is an inherited autosomal recessive disease of skeletal muscle caused by a mutation in the TRIM32 gene. Currently its pathogenesis is entirely unclear. Typically the regeneration process of adult skeletal muscle during growth or following injury is con...

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Autors principals: Nicklas, Sarah, Otto, Anthony, Wu, Xiaoli, Miller, Pamela, Stelzer, Sandra, Wen, Yefei, Kuang, Shihuan, Wrogemann, Klaus, Patel, Ketan, Ding, Hao, Schwamborn, Jens C.
Format: Artigo
Idioma:Inglês
Publicat: Public Library of Science 2012
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Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC3267731/
https://ncbi.nlm.nih.gov/pubmed/22299041
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1371/journal.pone.0030445
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