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Acquired Omenn-Like Syndrome, a Novel Posttransplant Autoaggression Syndrome Reversed by Rapamycin

Graft-versus-host disease is uncommon in autologous hematopoietic cell transplantation (HCT) and is typically brief and mild. We report unusual, protracted, and severe Omenn syndrome-like autoaggression following autologous HCT. We identified a profound FOXP3(+) regulatory T cell defect that coincid...

Deskribapen osoa

Gorde:
Xehetasun bibliografikoak
Egile Nagusiak: Vinh, Donald C., Bin Dhuban, Khalid, Mason, Helen, Lejtenyi, Duncan, Jung, SungMi, Sheppard, Donald C., Faury, Damien, Jabado, Nada, Piccirillo, Ciriaco A.
Formatua: Artigo
Hizkuntza:Inglês
Argitaratua: American Society for Microbiology 2012
Gaiak:
Sarrera elektronikoa:https://ncbi.nlm.nih.gov/pmc/articles/PMC3255959/
https://ncbi.nlm.nih.gov/pubmed/22089244
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1128/CVI.05456-11
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