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Purine nucleoside phosphorylase deficiency with a novel PNP gene mutation: a first case report from India

The authors report a case of purine nucleoside phosphorylase (PNP) deficiency for the first time from India. The case presented with recurrent severe infections, developmental delays, seizures and progressive neurological deterioration. The diagnosis of primary immunodeficiency disorder was delayed...

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Detalhes bibliográficos
Main Authors: Madkaikar, Manisha Rajan, Kulkarni, Shilpa, Utage, Prashant, Fairbanks, Lynette, Ghosh, Kanjaksha, Marinaki, Anthony, Desai, Mukesh
Formato: Artigo
Idioma:Inglês
Publicado em: BMJ Publishing Group 2011
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC3238109/
https://ncbi.nlm.nih.gov/pubmed/22669887
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1136/bcr.09.2011.4804
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