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Hb E/beta-thalassaemia: a common & clinically diverse disorder

Haemoglobin E-beta thalassaemia (Hb E/β-thalassaemia) is the genotype responsible for approximately one-half of all severe beta-thalassaemia worldwide. The disorder is characterized by marked clinical variability, ranging from a mild and asymptomatic anaemia to a life-threatening disorder requiring...

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Detalhes bibliográficos
Main Authors: Olivieri, Nancy F., Pakbaz, Zahra, Vichinsky, Elliott
Formato: Artigo
Idioma:Inglês
Publicado em: Medknow Publications & Media Pvt Ltd 2011
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC3237252/
https://ncbi.nlm.nih.gov/pubmed/22089616
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