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A CASE OF DYSKERATOSIS CONGENITA WITH PRIMARY AMENORRHEA AND ADENOCARCINOMA OF STOMACH

Dyskeratosis congenita (DC) is a rare disease characterized by hyperpigmentation, nail dystrophy and mucous membrane abnormality. Commonly occurring in males, the patients die young usually due to bone marrow suppression. Malignancies of various descriptions have been reported in this disease, the c...

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Autors principals: Chakrabarti, Nandini, Sarma, Nilendu, Chattopadhyay, Chandan, Chowdhuri, Atanu Roy, Das, Chanchal, Pal, Salil K
Format: Artigo
Idioma:Inglês
Publicat: Medknow Publications & Media Pvt Ltd 2011
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC3221235/
https://ncbi.nlm.nih.gov/pubmed/22121290
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.4103/0019-5154.87167
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