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Loss of Mecp2 in Substantia Nigra Dopamine Neurons Compromises the Nigrostriatal Pathway

Mutations in the methyl-CpG-binding protein 2 (MeCP2) result in Rett syndrome (RTT), an X-linked disorder that disrupts neurodevelopment. Girls with RTT exhibit motor deficits similar to those in Parkinson's disease, suggesting defects in the nigrostriatal pathway. This study examined age-depen...

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Autors principals: Gantz, Stephanie C., Ford, Christopher P., Neve, Kim A., Williams, John T.
Format: Artigo
Idioma:Inglês
Publicat: Society for Neuroscience 2011
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Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC3201707/
https://ncbi.nlm.nih.gov/pubmed/21880923
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1523/JNEUROSCI.0684-11.2011
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