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Partial Requirement of Endothelin Receptor B in Spiral Ganglion Neurons for Postnatal Development of Hearing

Impairments of endothelin receptor B (Ednrb/EDNRB) cause the development of Waardenburg-Shah syndrome with congenital hearing loss, hypopigmentation, and megacolon disease in mice and humans. Hearing loss in Waardenburg-Shah syndrome has been thought to be caused by an Ednrb-mediated congenital defe...

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Detalhes bibliográficos
Main Authors: Ida-Eto, Michiru, Ohgami, Nobutaka, Iida, Machiko, Yajima, Ichiro, Kumasaka, Mayuko Y., Takaiwa, Kazutaka, Kimitsuki, Takashi, Sone, Michihiko, Nakashima, Tsutomu, Tsuzuki, Toyonori, Komune, Shizuo, Yanagisawa, Masashi, Kato, Masashi
Formato: Artigo
Idioma:Inglês
Publicado em: American Society for Biochemistry and Molecular Biology 2011
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Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC3191003/
https://ncbi.nlm.nih.gov/pubmed/21715336
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1074/jbc.M111.236802
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