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Reversible aggregation of PABPN1 pre-inclusion structures

Increased aggregation of misfolded proteins is associated with aging, and characterizes a number of neurodegenerative disorders caused by homopolymeric amino acid expansion mutations. PABPN1 is an aggregation-prone nuclear protein. Natural aggregation of wild-type (WT) PABPN1 is not known to be dise...

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Main Authors: Raz, Vered, Abraham, Tsion, van Zwet, Erik W, Dirks, Roeland W, Tanke, Hans J, van der Maarel, Silvère M
Formato: Artigo
Idioma:Inglês
Publicado: Landes Bioscience 2011
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Acceso en liña:https://ncbi.nlm.nih.gov/pmc/articles/PMC3149881/
https://ncbi.nlm.nih.gov/pubmed/21818414
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.4161/nucl.2.3.15736
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