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A Case of Thrombotic Thrombocytopenia Purpura Associated with Systemic Lupus Erythematosus: Diagnostic Utility of ADAMTS-13 Activity

Thrombotic thrombocytopenia purpura (TTP) caused by a deficiency in ADAMTS-13 activity is considered to involve a subset of thrombotic microangiopathy (TMA). Although concept of TTP is included under the umbrella of TMA, discrimination of TTP from TMA is occasionally difficult in an autoimmune disor...

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Autores principales: Yamada, Risa, Nozawa, Kazuhisa, Yoshimine, Takashi, Takasaki, Yoshinari, Ogawa, Hideoki, Takamori, Kenji, Sekigawa, Iwao
Formato: Artigo
Lenguaje:Inglês
Publicado: SAGE-Hindawi Access to Research 2011
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC3138087/
https://ncbi.nlm.nih.gov/pubmed/21776377
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.4061/2011/483642
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