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Idiopathic Pulmonary Fibrosis: Update on Genetic Discoveries

Idiopathic pulmonary fibrosis (IPF) is a progressive fibrotic disease of the lungs that increases in prevalence with advanced age. Recent evidence indicates that mutations in genes of two different biologic pathways lead to the common phenotype of familial pulmonary fibrosis (FPF) and sporadic IPF....

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Detalles Bibliográficos
Autor Principal: Garcia, Christine Kim
Formato: Artigo
Idioma:Inglês
Publicado: American Thoracic Society 2011
Assuntos:
Acceso en liña:https://ncbi.nlm.nih.gov/pmc/articles/PMC3131833/
https://ncbi.nlm.nih.gov/pubmed/21543794
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1513/pats.201008-056MS
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