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Idiopathic Pulmonary Fibrosis: Update on Genetic Discoveries

Idiopathic pulmonary fibrosis (IPF) is a progressive fibrotic disease of the lungs that increases in prevalence with advanced age. Recent evidence indicates that mutations in genes of two different biologic pathways lead to the common phenotype of familial pulmonary fibrosis (FPF) and sporadic IPF....

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Autor principal: Garcia, Christine Kim
Format: Artigo
Idioma:Inglês
Publicat: American Thoracic Society 2011
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC3131833/
https://ncbi.nlm.nih.gov/pubmed/21543794
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1513/pats.201008-056MS
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