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Idiopathic Pulmonary Fibrosis: Update on Genetic Discoveries
Idiopathic pulmonary fibrosis (IPF) is a progressive fibrotic disease of the lungs that increases in prevalence with advanced age. Recent evidence indicates that mutations in genes of two different biologic pathways lead to the common phenotype of familial pulmonary fibrosis (FPF) and sporadic IPF....
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| Главный автор: | |
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| Формат: | Artigo |
| Язык: | Inglês |
| Опубликовано: |
American Thoracic Society
2011
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| Предметы: | |
| Online-ссылка: | https://ncbi.nlm.nih.gov/pmc/articles/PMC3131833/ https://ncbi.nlm.nih.gov/pubmed/21543794 https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1513/pats.201008-056MS |
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