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Bone Mass in Rett Syndrome: Association with Clinical Parameters and MECP2 Mutations

Rett Syndrome (RTT) is an X-linked neurodevelopmental disorder caused by mutations in the MECP2 gene. In 49 female RTT children, ages 1.9–17 years, bone mass was assessed and correlated with clinical parameters and mutations involving the MECP2 gene. We also studied 5 adult females, ages 20–33 years...

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Autors principals: Shapiro, Jay R., Bibat, Genila, Hiremath, Girish, Blue, Mary E., Hundalini, Shilpa, Yablonski, Theodore, Kantipuly, Aditi, Rohde, Charles, Johnston, Michael, Naidu, SakkuBai
Format: Artigo
Idioma:Inglês
Publicat: 2010
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Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC3074246/
https://ncbi.nlm.nih.gov/pubmed/20661168
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1203/PDR.0b013e3181f2edd2
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